ORAK HÜCRE ANEMİ KRİZİNE SEKONDER BİLATERAL FEMUR BAŞI OSTEONEKROZUNUN KEMİK SİNTİGRAFİSİ İLE DEĞERLENDİRİLMESİ

Füsun Aydoğan, Erhan Yengil, Nilgül Üstün, Raif Özden, Mehmet Rami Helvacı
1.420 348

Öz


Orak hücreli anemi (Sicklecellanemia)
hemoglobin S olarak adlandırılan anormal
hemoglobinlerin sebeb olduğu herediter geçişli
hastalık olarak tanımlanmaktadır. Orak hücre
anemi krizinde genellikle göğüste, kemiklerde
ve abdomendeki kapillerlerin morfolojisi
bozulmuş eritrositler tarafından tıkanmasıyla
meydana gelen infarktlar oluşur. Bu vaka
takdimindeorak hücre anemisi bulunan ve bir
aydır devam eden yürümekte zorluk ve ağrı
şikayeti bulunan 29 yaşında erkek hasta
sunulmuştur.
Anahtar Kelimeler: Orak hücre anemisi,
Kemik Sintigrafisi, Vasooklisiv Kriz


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